Case Report

An uncommon cause of isolated ascites: Pseudomyxoma peritonei

Louly Hady*, I Nassar, K Znati and N Kabbaj

Published: 26 April, 2019 | Volume 3 - Issue 1 | Pages: 001-005

Pseudomyxoma peritonei (PMP) or Gelatinous Peritoneal Disease is a rare condition that refers to an anatomo-clinical entity characterized by ascites of variable abundance in the peritoneal cavity, viscous or mucinous, associated or not with neoplastic epithelial cells. It predominates in women. Diagnosis is guided by imaging and confirmed by histology. Prognosis is good in case of early management. We report the case of a male diagnosed with Pseudomyxoma peritonei revealed by isolated ascites.

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Ascites; Appendix mucocele; Pseudomyxoma peritonei


  1. Shih IM, Yan H, Speyrer D, Shmookler BM, Sugarbaker PH, et al. Molecular genetic analysis of appendiceal mucinous adenomas in identical twins, including one with pseudomyxoma peritonei. Am J Surg Pathol. 2001; 25: 1095-1099. Ref.: https://tinyurl.com/y2ks76zw
  2. Smeenk RM, van Velthuysen ML, Verwaal VJ, Zœtmulder FA. Appendiceal neoplasms and pseudomyxoma peritonei: a popu- lation based study. Eur J Surg Oncol. 2008; 4: 196-201. Ref.: https://tinyurl.com/y5x4qr2h
  3. Elias D, Gilly F, Quenet F, Bereder JM, Sidéris L, et al. Pseudomyxoma peritonei: a French multicentric study of 301 patients treated with cytoreductive surgery and intraperi- toneal chemotherapy. Eur J Surg Oncol. 2010; 36: 456-462. Ref.: https://tinyurl.com/yy3w6cl6
  4. Moran BJ, Cecil TD. The etiology, clinical presentation, and management of pseudomyxoma peritonei. Surg Oncol Clin N Am. 2003; 12: 585–603. Ref.: https://tinyurl.com/y5z72s2j
  5. Esquivel J. Sugarbaker PH. Clinical presentation of pseudomyxoma peritonei syndrome. Br J Surg. 2000; 87: 1414–1418. Ref.: https://tinyurl.com/y48vnspq
  6. Smeenk RM, Bruin SC, van Velthuysen ML, Verwaal VJ. Pseudomyxoma peritonei. Curr Probl Surg. 2008; 45: 527-575. Ref.: https://tinyurl.com/y4yskvch
  7. Fallis SA, Moran BJ. Management of pseudomyxoma peritonei. J BUON. 2015; 20: S47–S55. Ref.: https://tinyurl.com/y2pmyarq
  8. Sulkin TV, O’Neill H, Amin AI, Moran B. CT in pseudomyxoma peritonei: a review of 17 cases. Clin Radiol. 2002; 57: 608-613. Ref.: https://tinyurl.com/y38dv33k
  9. Passot G, Glehen O, Pellet O, Isaac S, Tychyj C, et al. Pseudomyxoma peritonei: role of 18F-FDG PET in preo- perative evaluation of pathological grade and potential for complete cytoreduction. Eur J Surg Oncol. 2010; 36: 315-323. Ref.: https://tinyurl.com/yxscjfw7
  10. Koh JL, Liauw W, Chua T, Morris DL. Carbohydrate anti- gen 19-9 (CA 19-9) is an independent prognostic indicator in pseudomyxoma peritonei post cytoreductive surgery and per- ioperative intraperitoneal chemotherapy. J Gastrointest Oncol. 2013; 4: 173-181. Ref.: https://tinyurl.com/y52ahtms
  11. Carmignani CP, Hampton R, Sugarbaker CE, Chang D, Sugarbaker PH. Utility of CEA and CA 19-9 tumor markers in diagnosis and prognostic assesment of mucinous epithelial cancer of the appendix. J Surg Oncol. 2004; 87: 162-166. Ref.: https://tinyurl.com/y5aaxwrt
  12. Dartigues P, Isaac S, Villeneuve L, Glehen G, Capovilla M, et al. Mise au point sur le pseudo-myxome péritonéal. Aspects anatomopathologiques, et implications thérapeutiques. Ann Pathol. 2014; 34: 14–25. Ref.: https://tinyurl.com/y5beavaw
  13. Sugarbaker PH. Surgical treatment of peritoneal carcinomatosis: 1988 Du Pont lecture. Can J Surg. 1989; 32: 164-170. Ref.: https://tinyurl.com/yxlz9h6a
  14. Moran B, Baratti D, Yan TD, Kusamura S, Deraco M. Consensus statement on the loco-regional treatment of appendiceal muci- nous neoplasms with peritoneal dissemination (pseudomyxoma peritonei). J Surg Oncol. 2008; 98: 277-282. Ref.: https://tinyurl.com/yy5hsfuh
  15. Yan TD, Bijelic L, Sugarbaker PH. Critical analysis of treatment failure after complete cytoreductive surgery and perioperative intraperitoneal chemotherapy for peritoneal dissemination from appendiceal mucinous neoplasms. Ann Surg Oncol. 2007; 14: 2289-2299. Ref.: https://tinyurl.com/y5xowepd
  16. Chua TC, Moran BJ, Sugarbaker PH, Levine EA, Glehen O, et al. Early- and long-term outcome data of patients with pseudomyxoma peritonei from appendiceal origin treated by a strategy of cytoreductive surgery and hyperthermic intraperitoneal chemotherapy. J Clin Oncol. 2012; 30: 2449-2456. Ref.: https://tinyurl.com/yxftnuzu


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